Congenital High Airway Obstruction Syndrome (CHAOS): Prenatal Diagnosis and Perinatal Intervention – A Case Report
Keywords:Airway Obstruction, Ex utero intrapartum treatment, Larynx, Prenatal ultrasonography
Congenital high airway obstruction syndrome (CHAOS) is a rare life-threatening fetal anomaly which occurs as a result of either partial or complete obstruction of the upper fetal airway. Prenatal recognition is important for multidisciplinary team management. We present a case with CHAOS diagnosed antenatal imaging and the baby was delivered via ex utero intrapartum treatment (EXIT) procedure. The airway managed to be secured via tracheostomy while maintaining the fetus on feto-placental circulation. However, oxygen saturation started to decline despite successfully securing the upper airway. Unfortunately, we lost the baby despite active resuscitation possibly due to insufficient lung function secondary to chronic obstruction prenatally.
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