Congenital High Airway Obstruction Syndrome (CHAOS): Prenatal Diagnosis and Perinatal Intervention – A Case Report

Authors

  • Addina Mohd Baki Department of Otorhinolaryngology - Head and Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia , Kelantan, Malaysia
  • Wan Nur Anis Wan Draman Department of Otorhinolaryngology-Head & Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, Kelantan, Malaysia
  • Hashimah Ismail Department of Otorhinolaryngology-Head & Neck Surgery, Hospital Raja Perempuan Zainab 2, Kelantan, Malaysia
  • Irfan Mohamad Department of Otorhinolaryngology-Head & Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, Kelantan, Malaysia

DOI:

https://doi.org/10.51407/mjpch.v28i1.170

Keywords:

Airway Obstruction, Ex utero intrapartum treatment, Larynx, Prenatal ultrasonography

Abstract

Congenital high airway obstruction syndrome (CHAOS) is a rare life-threatening fetal anomaly which occurs as a result of either partial or complete obstruction of the upper fetal airway. Prenatal recognition is important for multidisciplinary team management. We present a case with CHAOS diagnosed antenatal imaging and the baby was delivered via ex utero intrapartum treatment (EXIT) procedure. The airway managed to be secured via tracheostomy while maintaining the fetus on feto-placental circulation. However, oxygen saturation started to decline despite successfully securing the upper airway.  Unfortunately, we lost the baby despite active resuscitation possibly due to insufficient lung function secondary to chronic obstruction prenatally.

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References

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Published

2022-06-30

How to Cite

Mohd Baki, A., Wan Draman, W. N. A. ., Ismail, . H. ., & Mohamad, I. (2022). Congenital High Airway Obstruction Syndrome (CHAOS): Prenatal Diagnosis and Perinatal Intervention – A Case Report. Malaysian Journal of Paediatrics and Child Health, 28(1), 84-90. https://doi.org/10.51407/mjpch.v28i1.170

Issue

Section

Case Report