Acute Respiratory Distress in the Newborn: Congenital Nasal Pyriform Aperture Stenosis the Underlying Pathology

Authors

  • Liyana Ghazali Department of Otorhinolaryngology-Head Neck Surgery School of Medical Sciences Universiti Sains Malaysia Health Campus, Malaysia
  • Addina Mohd Baki Department of Otorhinolaryngology, Hospital Raja Perempuan Zainab II, Kelantan, Malaysia
  • Hashimah Ismail Department of Otorhinolaryngology, Hospital Raja Perempuan Zainab II, Kelantan, Malaysia
  • Azliana Aziz Department of Otorhinolaryngology-Head Neck Surgery School of Medical Sciences, Universiti Sains Malaysia, 16150 Kubang Kerian, Kelantan, Malaysia

DOI:

https://doi.org/10.51407/mjpch.v28i1.155

Keywords:

Congenital Pyriform Aperture Stenosis, Neonate, Airway Obstruction, Nasolabial Approach

Abstract

Congenital nasal pyriform aperture stenosis (CNPAS) is a rare cause of neonatal upper airways obstruction. It can occur as an isolated anomaly or be associated with other cranial-facial defects. Clinically, CNPAS manifests as apneic crises, episodic cyanosis, and difficulty in feeding. Here we report a newborn developing respiratory distress after birth that required oxygen support and was confirmed diagnosis of CNPAS by computed tomography (CT) scan. The newborn had successfully undergone surgical intervention via the nasolabial approach.

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Published

2022-06-21

How to Cite

Ghazali, L., Mohd Baki, A., Ismail, H., & Aziz, A. (2022). Acute Respiratory Distress in the Newborn: Congenital Nasal Pyriform Aperture Stenosis the Underlying Pathology. Malaysian Journal of Paediatrics and Child Health, 28(1), 44-50. https://doi.org/10.51407/mjpch.v28i1.155

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Section

Case Report

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